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1.
Arch. argent. pediatr ; 121(6): e202202853, dic. 2023. ilus
Article in English, Spanish | LILACS, BINACIS | ID: biblio-1518733

ABSTRACT

Se informa de un lipoblastoma perineal en una niña de 5 años localizado en el labio mayor derecho. La lesión aumentó gradualmente en 6 meses. En la ecografía y la resonancia magnética (RM), se observó un tumor heterogéneo sólido limitado con componente graso. Tras su extirpación quirúrgica, el estudio anatomopatológico confirmó un lipoblastoma. El lipoblastoma es un tumor mesenquimatoso benigno poco frecuente de la lactancia y la primera infancia. Los síntomas varían en función de la localización; pueden observarse signos de compresión de los órganos adyacentes. Este tipo de tumores inusuales de los tejidos blandos son más frecuentes en menores de 3 años. Los lipoblastomas se localizan predominantemente en las extremidades, pero también pueden encontrarse en la cabeza y el cuello, el tronco, el mediastino, el riñón, el mesenterio, el retroperitoneo y el perineo. Se debe sospechar su presencia en función de los hallazgos de la ecografía y la RM.


We reported a perineal lipoblastoma in a 5-year-old girl located in the right labia mayor. The lesion gradually increased within 6 months. Ultrasound and magnetic resonance imaging (MRI) showed a limited solid heterogenous tumor with fatty component. After it had been surgically removed, the anatomopathological examination confirmed that it was a lipoblastoma. Lipoblastoma is a rare benign mesenchymal tumor of infancy and early childhood. Symptoms vary depending on localization; signs of compression of adjacent organs may be seen. This type of unusual soft tissue tumors occurred most often in under 3 years old. The localization of lipoblastomas is predominantly in the extremities but may be also found in other sites including the head and neck, trunk, mediastinum, kidney, mesentery, retropritoneum and perineum. The suspicion should be considered according to ultrasound and MRI findings.


Subject(s)
Humans , Female , Child, Preschool , Soft Tissue Neoplasms , Lipoblastoma/surgery , Lipoblastoma/diagnosis , Lipoblastoma/pathology , Magnetic Resonance Imaging , Kidney/pathology , Neck/pathology
2.
Article | IMSEAR | ID: sea-222169

ABSTRACT

Lipoblastoma is a rare, benign, rapidly growing tumor. These lesions are usually asymptomatic or symptomatic due to the compression of surrounding structures. The majority of them were diagnosed in early childhood. We report the case of a 2 years old boy with giant anterior mediastinal lipoblastoma who was apparently asymptomatic except for persistent fast berating. The mass was diagnosed by computed tomography-guided needle biopsy and confirmed after removal by thoracotomy

3.
Annals of Dentistry ; : 47-51, 2021.
Article in English | WPRIM | ID: wpr-906578

ABSTRACT

@#The presence of lobulated tumour arising from immature adipose tissue is called lipoblastoma when occurring as localised or discrete lesion, and lipoblastomatosis when spread diffusely. The purpose of this case study is to report a case of an 18 – year old man who presented with lipoblastoma in the left sublingual space which was found to be in close proximity with the left sublingual gland. Magnetic resonance imaging (MRI) was taken and showed the tumour was confined within the sublingual space and no penetration was noted inferiorly through the mylohyoid muscle. Tumour dimension measured clinically was 3 cm x 2 cm x 2 cm and the anterior margin of the tumour crossed the midline and entered into the right sublingual space. Complete excision with sparing of neurovascular bundle was performed under general anaesthesia. Follow-up of 2 months showed complete remission of the lesion without any complications.

4.
Oncología (Guayaquil) ; 30(1): 31-38, Abril. 2020.
Article in Spanish | LILACS | ID: biblio-1140897

ABSTRACT

Introducción: El lipoblastoma es una neoplasia benigna de presentación infrecuente originada en el tejido adiposo, de presentación casi exclusiva en pacientes pediátricos antes de los tres años de edad, con predominio en el sexo masculino. Se localiza principalmente en las extremidades y tronco, como una tumoración indolora de crecimiento progresivo. El tratamiento de elección es quirúrgico y tiene pronóstico favorable. Las recidivas se presentan en los casos en los que la resección no pudo ser completa. Caso clínico: Lactante mujer de 7 meses de edad. Desde los tres meses de edadpresentó aumento progresivo del volumen de la extremidad inferior izquierda.Al examen físico se evidenciógran tumoraciónde 12 x 7 centímetrosque compromete la cara posterior del muslo izquierdo: Masa indolora y bien delimitada. Sin compromiso de la movilidad, sin edema de miembro. Taller diagnóstico: La Resonancia Magnética reportó unatumoración sólida de muslo izquierdo hiper-intensa en T1 y T2, hipo-intensa en STIR con septos finos en su interior, se extiende desde el musculo abductor magno del bíceps femoral y mide 11.2 x 7.9 x 8.4 cm en sus ejes longitudinal, anteroposterior y transversal respectivamente, desplazando y comprimiendo a los músculos semitendinoso, semimembranoso y gracilis. La paciente fue sometida a escisión completa y amplia de la masa, mediante abordaje posterolateral. Desenlace:Patología reportóun tumor constituido por tejido adiposo con tejido mixoide,sin atipia nuclear; se evidencia infiltración parcial del musculo esquelético adyacente, sin afectación de piel, sin necrosisy bordes quirúrgicos negativos para neoplasia. Inmunohistoquímica con marcador de proliferación celular KI-67 resultado positivo de 1%, y estudio de MDM2 (inhibidor de la activación transcripcional de p53) negativo; hallazgos compatibles con lipoblastoma. El estudio citogenético no fue realizado. Evolución: La paciente fue dada de alta al cuarto día post-operatorio sin complicaciones. Con una recuperación completa, en el quinto mes de seguimiento se realizónuevo estudio de resonancia magnética en la cual no se visualizan imágenes que sugieran tumor residual ni recidiva tumoral. Conclusión: El lipoblastoma debe ser tomada en cuenta como diagnóstico diferencial en niños con tumores de partes blandas, su tratamiento es eminentemente quirúrgico con un buen pronóstico si la extirpación es completa


Introduction: Lipoblastoma is an infrequent benign neoplasm originating in adipose tissue, presenting almost exclusively in pediatric patients before the age of three years, predominantly in males. It is located mainly on the limbs and trunk, as a painless, progressively growing tumor. The treatment of choice is surgical and has a favorable prognosis. Recurrences occur in cases in which the resection could not be complete. Clinical case: 7-month-old female infant. From the age of three months, he presented a progressive increase in the volume of the left lower limb. Physical examination revealed a large mass measuring 12 x 7 centimeters that involves the posterior aspect of the left thigh: a painless and well-defined mass. No compromise of mobility, no limb edema. Diagnostic workshop: Magnetic resonance imaging reported a hyper-intense solid tumor of the left thigh in T1 and T2, hypo-intense in STIR with fine septa inside it, extending from the abductor magnus muscle of the biceps femoris and measuring 11.2 x 7.9 x 8.4 cm in its longitudinal, anteroposterior and transverse axes respectively, displacing and compressing the semitendinosus, semimembranosus and gracilis muscles. The patient underwent a complete and wide excision of the mass using a posterolateral approach. Outcome: Pathology reported a tumor made up of adipose tissue with myxoid tissue, without nuclear atypia; partial infiltration of the adjacent skeletal muscle is evidenced, without skin involvement, without necrosis and negative surgical margins for neoplasia. Immunohistochemistry with a cell proliferation marker KI-67, a positive result of 1%, and a negative MDM2 study (inhibitor of transcriptional activation of p53); findings consistent with lipoblastoma. The cytogenetic study was not performed. Evolution:The patient was discharged on the fourth postoperative day without complications. With a complete recovery, in the fifth month of follow-up a new magnetic resonance study was performed in which no images that suggest residual tumor or tumor recurrence are visualized Conclusion: Lipoblastoma should be taken into account as a differential diagnosis in children with soft tissue tumors, its treatment is eminently surgicalwith a good prognosis if the removal is complete


Subject(s)
Humans , Chromosome Aberrations , Lipoblastoma , Infant , Case Reports
5.
Rev. chil. pediatr ; 91(2): 244-250, abr. 2020. graf
Article in Spanish | LILACS | ID: biblio-1098898

ABSTRACT

Resumen: Objetivo: Describir dos casos de lipoblastoma mediastínico, patología de baja incidencia y poco conocida, siendo aún más infrecuente en mediastino, sin haber reportes descritos en nuestro país. Casos Clínicos: 2 pacientes, ambos de sexo masculino, menores de 3 años, en los que se encontró como ha llazgo incidental una masa mediastínica en una radiografía de tórax. El estudio se complementó con una tomografía computada y en uno de los pacientes con una biopsia toracoscópica. En ambos se logró ex tirpación completa de la lesión vía toracotomía, siendo apoyado vía toracoscópica previa a la extracción de la lesión en uno de ellos. Uno de los pacientes evolucionó con Síndrome de Claude Bernard Horner el cual resolvió de manera espontánea luego de dos años y el segundo caso no presentó complicaciones. Conclusiones: el lipoblastoma mediastínico es una patología muy poco frecuente, las descripciones de la literatura se asemejan a los casos expuestos en este artículo, concluyendo que presentan un patrón muy similar entre ellos. Teniendo un pronóstico favorable si se logra la resección completa y siendo fundamental diferenciarlo de sus diagnósticos diferenciales para descartar malignidad.


Abstract: Objective: To describe two cases of mediastinal lipoblastoma, an infrequent and little-known patho logy, which is extremely rare in the mediastinum, with no cases reported in our country. Clinical Cases: Two case reports. Both patients were boys younger than three years, in which a mediastinal mass was found incidentally on a chest x-ray. The study was complemented with a CT scan and with a thoracoscopic biopsy in one of the cases. Complete resection of the tumor was achieved in both patients through thoracotomy. One of the patients presented Claude Bernard Horner syndrome as a complication from surgery, which resolved spontaneously after two years and the second case had no complications. Conclusion: Mediastinal lipoblastoma is a very rare pathology. Descriptions found in existing literature are similar to the cases presented in this article. We can conclude that mediastinal lipoblastomas in pediatrics present a very similar pattern and presentation, having a good prognosis if complete resection is achieved. Also, it is essential to distinguish it from its differential diagnoses in order to rule out malignancy.


Subject(s)
Humans , Male , Infant , Child, Preschool , Tomography, X-Ray Computed , Lipoblastoma/diagnostic imaging , Mediastinal Neoplasms/diagnostic imaging , Thoracotomy , Lipoblastoma/surgery , Mediastinal Neoplasms/surgery
6.
Korean Journal of Head and Neck Oncology ; (2): 25-27, 2019.
Article in Korean | WPRIM | ID: wpr-787520

ABSTRACT

Lipoblastoma is a rare benign tumor with 80–90% occurring in children less than 3 years of age and 40% occurring in children less than 1 year of age. The most common site of incidence is limb, and then trunk. Neck is the rare site of incidence. The main symptom that the patient complains about is a rapidly growing neck mass without pain. When the size of mass increases, it can cause dyspnea, Horner's syndrome. Lipoblastoma is usually diagnosed as a lipoma in the fine needle aspiration. Since it is not differentiated from lipoma, liposarcoma, and hibernating adenoma in CT and MRI, the definitive diagnosis is histologic diagnosis through surgical resection. The treatment is complete surgical resection. And recurrence rate is 9–25% due to incomplete resection. Authors report this case with a review of literatures since we experienced a case of lipoblastoma diagnosed histopathologically after surgical treatment of neck mass.


Subject(s)
Child , Humans , Adenoma , Biopsy, Fine-Needle , Diagnosis , Dyspnea , Extremities , Horner Syndrome , Incidence , Lipoblastoma , Lipoma , Liposarcoma , Magnetic Resonance Imaging , Neck , Pediatrics , Recurrence
7.
Arch. argent. pediatr ; 116(1): 139-142, feb. 2018. ilus
Article in Spanish | LILACS, BINACIS | ID: biblio-887446

ABSTRACT

El lipoblastoma forma parte de los tumores derivados del tejido adiposo. Es una neoplasia benigna que se puede presentar de forma localizada o difusa, que afecta a niños en la primera infancia y que, generalmente, se localiza en el tronco y las extremidades. Estos tumores son poco frecuentes en la edad pediátrica, pero cuando uno de ellos se presenta, constituye un desafío que se debe resolver rápidamente por el riesgo de malignidad que implican otras lesiones neoplásicas, de similares características. El diagnóstico preoperatorio es dificultoso, ya que los métodos por imágenes no aportan información específica que permita diferenciarlos de otros tumores, como los liposarcomas. El diagnóstico definitivo es anatomopalógico y, en casos dudosos, es necesaria la confirmación citogenética. Se presenta el caso de un niño de 14 meses de edad con diagnóstico de lipoblastoma de localización retroperitoneal de gran tamaño.


Lipoblastoma is part of tumors derived from adipose tissue. It is a benign neoplasm that can be localized or diffuse, affecting children in early childhood and usually located in the trunk and extremities. These tumors are uncommon in the pediatric age, but when one of them is present, it is a challenge that we must resolve quickly due to the risk of malignancy that involves other similar neoplastic lesions. The preoperative diagnosis is difficult, because the imaging methods do not provide specific information that allows us to differentiate them from other tumors, such as liposarcomas. The definitive diagnosis is anatomopathological and, in doubtful cases, cytogenetic confirmation is necessary. We present the case of a 14-month-old boy with diagnosis of large sized lipoblastoma of retroperitoneal localization.


Subject(s)
Humans , Male , Infant , Retroperitoneal Neoplasms/pathology , Lipoblastoma/pathology , Tumor Burden
8.
Rev. chil. pediatr ; 87(3): 199-203, jun. 2016. ilus, tab
Article in Spanish | LILACS | ID: lil-787104

ABSTRACT

Introducción El lipoblastoma es una neoplasia benigna del tejido adiposo, de presentación infrecuente y casi exclusiva en niños menores de 3 años. Usualmente se presenta en las extremidades como una masa indolora de crecimiento progresivo, estableciéndose su diagnóstico definitivo mediante análisis histológico y citogenético. Objetivo Presentar un caso clínico de lipoblastoma de ubicación inhabitual en una lactante y revisar la literatura al respecto. Caso clínico Lactante mayor de 16 meses, con aumento de volumen abdominal de 6 meses de evolución, asociado a una ingesta alimentaria disminuida, sin otros síntomas. El estudio de imagen reveló una imagen de aspecto lipoideo que comprometía casi la totalidad de la cavidad abdominal, muy sugerente de lipoblastoma, realizándose la resección de un tumor retroperitoneal de 18 cm de diámetro que rechazaba los órganos vecinos. El análisis histológico fue suficiente para confirmar el diagnóstico. En el seguimiento no hubo recidiva. Conclusión Tomando en cuenta la baja frecuencia de esta afección y su inusual presentación, se reporta el caso de esta paciente, para considerarlo dentro del diagnóstico diferencial de masa abdominal en un lactante.


Introduction Lipoblastoma is a benign neoplasia of the adipose tissue. It is a rare conditionand almost exclusively presents in children under 3 years old. It usually occurs in extremities as a painless volume increase of progressive growth, with the definitive diagnosis being established by pathological and cytogenetic analysis. The treatment of choice is complete resection, and follow-up period of up to five years is recommended due to a recurrence of up to 25%. Objective To present an unusual location of this uncommon condition in an infant, and review the related literature. Case report A sixteen-month child with an increase in abdominal growth of six-months progression, associated with a decreased food intake, and with no other symptoms. The imaging study revealed a lipoid-like image compromising almost the entire abdominal cavity, very suggestive of lipoblastoma. A resection was performed on an 18 cm diameter retroperitoneal tumour that rejected the adjacent organs. Histological analysis was enough to confirm diagnosis without the need for cytogenetic analysis. The follow-up showed no recurrence of the disease. Conclusion Given the rarity of this disease and its unusual presentation, we communicate this clinical case, in order to be considered in the differential diagnosis of abdominal mass in chilhood.


Subject(s)
Humans , Female , Infant , Retroperitoneal Neoplasms/diagnosis , Lipoblastoma/diagnosis , Retroperitoneal Neoplasms/surgery , Retroperitoneal Neoplasms/pathology , Follow-Up Studies , Disease Progression , Diagnosis, Differential , Lipoblastoma/surgery , Lipoblastoma/pathology
9.
Rev. bras. cir. plást ; 29(3): 319-323, jul.-sep. 2014. ilus
Article in English, Portuguese | LILACS | ID: biblio-711

ABSTRACT

O lipoblastoma é um tumor mesenquimal raro, composto de lipoblastos que continuam sua proliferação após o período pós-natal e que acometem, predominantemente, a população pediátrica. Apresenta prognóstico excelente, apesar do potencial de invasão local e do crescimento rápido. Os autores relatam o caso de uma paciente pediátrica portadora de volumosa lesão em antebraço direito, ocasionando importante comprometimento funcional do membro acometido. Aspectos relevantes no diagnóstico diferencial e manejo são discutidos neste trabalho, visto tratar-se de lesão com potencial risco incapacitante futuro, caso não manejada corretamente.


Lipoblastoma is a rare mesenchymal tumor occurring primarily in pediatric patients and formed by lipoblasts that proliferate after the postnatal period. Despite its potential for local invasion and rapid growth, its prognosis is excellent. In this study, we report the case of a pediatric patient with a ponderous lesion in the right forearm that caused considerable functional impairment of the affected limb. We also discuss the relevant aspects concerning the differential diagnosis and management of the disease, as it has the potential to cause incapacity without proper treatment.


Subject(s)
Humans , Female , Infant , History, 21st Century , Soft Tissue Neoplasms , Surgery, Plastic , Wounds and Injuries , Review Literature as Topic , Adipose Tissue , Adipocytes , Evaluation Study , Lipoma , Soft Tissue Neoplasms/surgery , Soft Tissue Neoplasms/pathology , Surgery, Plastic/methods , Wounds and Injuries/surgery , Adipose Tissue/embryology , Adipose Tissue/metabolism , Adipocytes/physiology , Adipocytes/metabolism , Lipoblastoma , Lipoblastoma/surgery , Lipoblastoma/pathology , Lipoma/surgery , Lipoma/pathology
10.
Journal of the Korean Association of Pediatric Surgeons ; : 58-61, 2014.
Article in Korean | WPRIM | ID: wpr-222027

ABSTRACT

Palpable inguinal mass in children should be differentiated from inguinal hernia, hydrocele, lymph node, and tumor. Though using ultrasonography, fatty tumor would be misdiagnosed as incarcerated inguinal hernia containing fatty component. We experienced the huge inguinal lipoblastoma in 5-year-old girl mimicking recurrent incarcerated hernia. Laparoscopic exploration revealed it was not incarcerated hernia but well demarcated bulging mass from abdominal wall. Mass was about 10x4x3 cm and extended from internal inguinal ring to saphenous opening. It was near total excised because of right external iliac vein injury. Pathologically, it was proven as lipoblastoma containing mature adipocyte with lipoblast and fibrous septa. Postoperatively, we noticed a segmental thrombotic occlusion of external iliac vein. After 1 year, she has no symptom related to occluded vessel. The remained lipoblastoma showed no interval change. Even lipoblastoma has a good prognosis with low recurrence rate, we need careful follow-up.


Subject(s)
Child , Child, Preschool , Female , Humans , Abdominal Wall , Adipocytes , Follow-Up Studies , Hernia , Hernia, Inguinal , Iliac Vein , Inguinal Canal , Lipoblastoma , Lipoma , Lymph Nodes , Prognosis , Recurrence , Ultrasonography
11.
Arq. bras. oftalmol ; 76(4): 244-246, jul.-ago. 2013. ilus
Article in Portuguese | LILACS | ID: lil-686563

ABSTRACT

O objetivo desse estudo é descrever uma criança com lipossarcoma periorbital, caracterizando seus aspectos clínico-epidemiológicos e terapêuticos. Menina de 6 meses de idade com tumoração crescente há dois meses em região fronto-zigomática direita, a qual foi submetida à exérese e cujas análises anatomopatológica (AP) e imuno-histoquímica (IH) observaram achados típicos de lipoblastoma. Após isso, apresentou mais três recidivas tumorais com diagnósticos similares. Um ano depois da última cirurgia, houve nova recorrência, porém, dessa vez, o resultado dos exames análises anatomopatológica e imuno-histoquímica foi de lipossarcoma, sendo, então, encaminhada para complementar o tratamento com radio e quimioterapia, sem novas lesões até o momento. Devido a sua raridade, geralmente o lipossarcoma não entra no diagnóstico diferencial em pacientes com massas orbitais, porém, por ser localmente agressivo, torna-se vital a pronta identificação e tratamento de forma a oferecer melhores resultados terapêuticos e influência sobre a qualidade de vida do paciente.


The purpose of this study is report a child with periorbital liposarcoma describing the clinical, epidemiological and therapeutic aspects. Six-months-old female baby with increasing tumor in the right fronto-zigomatic region wich was submitted to excision and the patologic and immunohistochemistry analisys observed typical findings of lipoblastoma. After that, there were three tumors relapse with the same diagnosis. One year after the last surgery there was a recurrence of the tumor but at this time the diagnosis was lipossarcoma and the patient was referred for additional treatment wilth radiotherapy and chemotherapy no new injuries so far Due to its rarity, liposarcoma usually does not enter the differencial diagnosis in the patients with orbital masses, however because of its local aggressiveess, it's vital the early identification and treatment to provide better therapeutic results and quality of life.


Subject(s)
Female , Humans , Infant , Liposarcoma/pathology , Orbital Neoplasms/pathology , Diagnosis, Differential , Liposarcoma/therapy , Neoplasm Recurrence, Local/pathology , Neoplasm Recurrence, Local/therapy , Orbital Neoplasms/therapy , Reoperation , Treatment Outcome
12.
Korean Journal of Dermatology ; : 134-137, 2012.
Article in Korean | WPRIM | ID: wpr-165119

ABSTRACT

Lipoblastoma is a rare, benign tumor arising from embryonic fat tissues that continue to proliferate in the postnatal period. So, lipoblastoma occurs almost exclusively in infants and children younger than 3 years of age. Published reports showed that 70~90% of cases occur before the age of 3. Histopathologically, lipoblastoma, mimicking liposarcoma, was composed of well-defined lobulated fat tissue with multilobulated lipoblasts, undifferentiated mesenchymal cells, such as stellate or spindle cells and minimal myxoid stromas. The diagnosis of lipoblastoma is important because its management differs from that of lipoma and liposarcoma. To our knowledge, there are only a few reports of lipoblastoma in the Korean dermatologic literature. Herein, we present an interesting and atypical case of lipoblastoma in 68-year-old woman.


Subject(s)
Aged , Child , Female , Humans , Infant , Lipoblastoma , Lipoma , Liposarcoma
13.
Korean Journal of Dermatology ; : 689-692, 2010.
Article in Korean | WPRIM | ID: wpr-210548

ABSTRACT

Lipoblastomas are rare benign tumors of infancy originating from embryonic fat cells that continue to proliferate in the postnatal period. Lipoblastomas usually affect children younger than 3 years of age. Lipoblastomas may mimic other infantile tumors, including hemangiomas, lymphangiomas, lipomas, and liposarcomas. A correct diagnosis is necessary to ensure appropriate treatment. We witnessed a case of a 5-month-old boy who presented with a very firm, round, well-circumscribed mass on the posterior part of the right lower leg. On magnetic resonance imaging, a hemangioma was suspected. However, histopathological examination revealed a lobulated adipose tissue composed of a mixture of immature multivacuolated lipoblasts and mature adipocytes without nuclear atypia. Based on the clinical and histopathological findings, the diagnosis of benign lipoblastoma was made.


Subject(s)
Child , Humans , Infant , Adipocytes , Adipose Tissue , Dietary Sucrose , Hemangioma , Hydrazines , Leg , Lipoblastoma , Lipoma , Liposarcoma , Lymphangioma , Magnetic Resonance Imaging , Wit and Humor as Topic
14.
Journal of Korean Medical Science ; : 1093-1096, 2010.
Article in English | WPRIM | ID: wpr-155852

ABSTRACT

We report a case of prenatally diagnosed congenital perineal mass which was combined with anorectal malformation. The mass was successfully treated with posterior sagittal anorectoplasty postnatally. On ultrasound examination at a gestational age of 23 weeks the fetal perineal mass were found on the right side. Any other defects were not visible on ultrasonography during whole gestation. Amniocentesis was performed to evaluate the fetal karyotyping and acetylcholinesterase which were also normal. As the fetus grew up, the mass size was slowly increased more and more. At birth, a female neonate had a perineal mass on the right side as expected. During operation, the anal sphincteric displacement was found near the mass and reconstructed through posterior sagittal incision. This is the first reported case of prenatally diagnosed congenital perineal mass, after birth which was diagnosed as lipoblastoma and even combined with anorectal malformation. This case shows that it can be of clinical importance to be aware of this rare fetal perineal mass in prenatal diagnosis and counseling.


Subject(s)
Adult , Female , Humans , Infant, Newborn , Male , Pregnancy , Amniocentesis , Anal Canal/abnormalities , Digestive System Abnormalities/diagnosis , Gestational Age , Lipoma/diagnosis , Perineum/pathology , Prenatal Diagnosis , Rectal Neoplasms/diagnosis , Rectum/abnormalities , Ultrasonography, Prenatal/methods
15.
The Korean Journal of Thoracic and Cardiovascular Surgery ; : 395-398, 2008.
Article in Korean | WPRIM | ID: wpr-13772

ABSTRACT

Lipoblastoma is a rare benign tumor that usually originates in children from the embryonic lipid cells of the extremities. This condition shows an early childhood occurrence, a benign nature without metastasis, a cellular composition of mainly mature lipid cells and an ability to differentiate into a simple lipoma. We have experienced a 15 month old girl who had developed a lipoblastoma in the right anterior mediastinum. Surgical resection was carried out without complications. Her postoperative course was uneventful. She has been well 6 months after the operation.


Subject(s)
Child , Humans , Extremities , Lipoblastoma , Lipoma , Mediastinal Neoplasms , Mediastinum , Neoplasm Metastasis
16.
The Korean Journal of Thoracic and Cardiovascular Surgery ; : 240-243, 2007.
Article in Korean | WPRIM | ID: wpr-209668

ABSTRACT

Mediastinal lipoblastoma is a rare benign tumor originating from embryonic lipid cells and it almost always occurs during infanthood or early childhood. It is a tumor with a good prognosis despite its potential for local invasion and rapid growth. We report here on a three years old girl who was treated for a benign lipoblastoma in the anterior mediastinum. CT scanning showed a fat containing mass without internal calcification or fluid component, and the mass showed a compressive effect on the adjacent structures. The mass was located between the pericardium and right mediastinal pleura and it was removed completely without complication. Pathologic examination revealed a benign lipoblastoma. The patient showed no evidence of recurrence at the time of the report.


Subject(s)
Female , Humans , Lipoblastoma , Mediastinum , Pericardium , Pleura , Prognosis , Recurrence , Tomography, X-Ray Computed
17.
Journal of the Korean Surgical Society ; : 166-169, 2007.
Article in Korean | WPRIM | ID: wpr-44381

ABSTRACT

Lipoblastoma is a relatively rare benign tumor that occurs in infancy and early childhood, and it arises from embryonic white fat. It is classified into two forms based on pathologic features: benign lipoblastoma is a superficial, well-defined mass and diffuse lipoblastomatosis is a deep, infiltrative lesion. They are both histologically benign, but local recurrences can happen without any tendency of metastasis. The prevalent sites are chiefly the upper and the lower extremities and less commonly the head, neck, trunk, mesentery, mediastinum, and retroperitoneum. The treatment of choice is surgical excisions, and the prognosis is good, but recurrence is possible in the case of incomplete excision, so wide local excision is preferred. We experienced a locally recurrent lipoblastoma in an 8 month old female child in the chest wall that reoccurred three months after the primary excision. Because 9th and 10th rib invasion was suspected on magnetic resonance imaging study, mass excision along with partial 9th and 10th ribs resection was performed. The histologic diagnosis confirmed lipoblastoma.


Subject(s)
Child , Female , Humans , Infant , Adipose Tissue, White , Diagnosis , Head , Lipoblastoma , Lower Extremity , Magnetic Resonance Imaging , Mediastinum , Mesentery , Neck , Neoplasm Metastasis , Prognosis , Recurrence , Ribs , Thoracic Wall , Thorax
18.
The Korean Journal of Thoracic and Cardiovascular Surgery ; : 395-397, 2007.
Article in Korean | WPRIM | ID: wpr-198855

ABSTRACT

Lipoblastoma is a rare benign mesenchymal tumor that occurs primarily in infancy and childhood. There are two types of lipoblastoma: focal or diffuse (lipoblastomatosis). This is typically located in the extremities, and less frequently in the trunk, head and neck, and the retroperitoneum. Lipoblastoma is a tumor with a good prognosis with no reported metastasis, despite of its potential for local invasion, local recurrence and rapid growth. Complete surgical resection is essential for treatment, and long term follow up is needed.


Subject(s)
Humans , Male , Extremities , Follow-Up Studies , Head , Lipoblastoma , Neck , Neoplasm Metastasis , Prognosis , Recurrence , Thoracic Wall , Thorax
19.
Journal of the Korean Association of Pediatric Surgeons ; : 179-186, 2007.
Article in Korean | WPRIM | ID: wpr-128470

ABSTRACT

Lipoblastoma is a rare benign soft tissue tumor occurring in infancy and early childhood. It is characterized by fat lobules with varying degrees of maturity, multivaculoated lipoblasts, fibrocapillary networks and myxoid stroma. Lipoblastoma has a good prognosis with no metastases despite its potential for local invasion. From Jan, 1990 through April, 2007, 12 children underwent the operation for lipoblastoma, 7 boys and 5 girls, diagnosed at median 22 months (5~43 months). Median follow up was 6 year 7 months. Primary sites included back (n=5), intraabdominal (n=2) and one in each of buttock, chest wall, neck, nose and scalp. Tumors presented with a growing mass in 9 patients, abdominal distension in 2, and an incidental finding on chest radiography in one. Complete excisions were done in all patients. There was one recurrence in a patient with a scalp mass. After reoperation, he has been doing well without evidence of recurrence. Lipoblastoma has a favorable prognosis, but recurrence can occur even with complete excision. Regular follow up is necessary to detect recurrences.


Subject(s)
Child , Female , Humans , Buttocks , Follow-Up Studies , Incidental Findings , Lipoblastoma , Neck , Neoplasm Metastasis , Nose , Prognosis , Radiography , Recurrence , Reoperation , Scalp , Thoracic Wall , Thorax
20.
Korean Journal of Otolaryngology - Head and Neck Surgery ; : 93-95, 2002.
Article in Korean | WPRIM | ID: wpr-646137

ABSTRACT

Lipoblastoma is a rare benign tumor of embryonal fat. This condition most often presents during childhood, before the age of 7 years, affects males more than females, and is typified by a slowly growing, usually subcutaneous mass arising in the limbs. Cases involving the head and neck are extremely rare. Our case arose in a 44-month-old male presenting with a rapidly enlarging soft lump in the right supraclavicular area. Diagnosis is by histology, and treatment of choice is complete surgical resection. We report one case of lipoblastoma in the neck with a review of the literature.


Subject(s)
Child , Child, Preschool , Female , Humans , Male , Diagnosis , Extremities , Head , Lipoblastoma , Neck
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